Majocchi's disease. Report of a pediatric case

Abstract

Introduction: Pigmented purpuric dermatoses include a group of benign, chronic diseases that are more common in adults and rarely reported in children. Among these is Majocchi's disease, or telangiectatic annular purpura, first described by Domenico Majocchi in 1896. It presents as annular, purpuric, telangiectatic, and hyperpigmented macules, most commonly on the lower extremities and buttocks. It predominates in women, adolescents, and young adults, with few reports in children. It is characterized by relapses and remissions, with lesions that can persist for years. Clinical case: A 6-year-old white male patient from a rural area, born of a normal pregnancy and delivery, with a history of allergies reported by his mother, for which he has been treated with antihistamines on an irregular basis. He was evaluated in a dermatology consultation about a year ago for hyperpigmented, purpuric lesions with slight petechial spotting, which sometimes vary in color from dark to lighter, without relief, do not disappear with finger pressure, and are predominant in the lower limbs up to the buttocks. Several hematological studies showed normal values, but there were disaggregated platelets with macroplatelets in the periphery. The dermatological study confirmed telangiectatic annular purpura or Majocchi's disease. Conclusions: This is a rare condition in pediatrics, with few reports in the literature, which is why it is important to raise awareness and disseminate information about it, especially among undergraduate and graduate students and other medical personnel, so that they are familiar with its clinical characteristics and diagnosis.